The swallowing disorder in myotonia dystrophica
نویسندگان
چکیده
منابع مشابه
Anaesthesia for major abdominal surgery in a patient with myotonia dystrophica.
A case report is presented of a woman with known myotonia dystrophica, who required partial gastric resection and cholecystectomy. Neuromuscular blockade was obtained using a single dose of vecuronium, and neuromuscular function was determined by the "train-of-four count" technique. The intraoperative course was uneventful, and it was not necessary to use neostigmine to antagonize neuromuscular...
متن کاملMyotonia dystrophica with heart involvement: an electron microscopic study of skeletal, cardiac, and smooth muscle.
The electron microscopic features of the striated skeletal muscle, the striated cardiac muscle, and the smooth muscle from a woman who had been suffering for many years from myotonia dystrophica with cardiac involvement are described. The skeletal muscle was studied at two different stages of the disease. In the first material the main changes consisted of centrally situated nuclei, disorganisa...
متن کاملSwallowing Disorder in Multiple Sclerosis: Modified Version of the Screening Tool
Objective: Dysphagia is commonly encountered in Multiple Sclerosis (MS). It can consequently cause severe complications such as the increased risk of dehydration, malnutrition and aspiration pneumonia that associated with an increased risk of death in the late stages of the disease. These complications can be prevented with an effective screening protocol. The Dysphagia in Multiple Sclerosis (D...
متن کاملMyotonia levior is a chloride channel disorder.
The group of dominant non-dystrophic myotonias, comprising disorders characterized by clinically similar forms of myogenic muscle stiffness, is genetically inhomogeneous. Dominant myotonia congenita (Thomsen's disease) is linked to CLCN1, the gene encoding the major muscle chloride channel, localized on chromosome 7q35. In contrast, dominant myotonias sensitive to potassium are caused by point ...
متن کاملNegative extradural pressure may not be caused by tenting of the dura.
Sir,—We read with interest the review article on anaesthesia and myotonia [1]. Myotonia dystrophica is an uncommon disorder with as yet no consensus of opinion regarding the ideal anaesthetic for these patients. Propofol has been used in this disorder with variable responses, including prolonged recovery, altered dose–response curves and precipitation of the myotonia. We report three additional...
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ژورنال
عنوان ژورنال: Gastroenterology
سال: 1966
ISSN: 0016-5085
DOI: 10.1016/s0016-5085(66)80031-8